无顶冠状静脉窦综合征(unroofed coronary sinus syndrome,UCSS)是一种较为复杂的先天性心脏畸形,本文报道了1例Kirklin分型Ⅳ型或者解剖分型Ⅲb型的患者,并结合手术及超声心动图资料分析了UCSS诊治的难点与要点。

Unroofed coronary sinus syndrome (UCSS) is a complicated congenital cardiac anomaly.This article reports a case of Kirklin type Ⅳ or anatomical classification type Ⅲb UCSS,and further discusses difficulties and key points of diagnosis and treatment of UCSS based on surgical and echocardiographic data.